Hearing loss is prevalent in major thalassemia but has not been reported in carrier alpha thalassemia. Here we present a case with alpha-thalassemia with deletion of homozygous traits that had bilateral sensorineural hearing loss which might have developed due to defect in the production of oxygen-carrying pigments. It is hypothesized that the poor oxygen carrying capacity of the blood supply in the cochlea may be possible cause of hearing loss. Here it can be emphasized that cases with thalassemia should be screened for hearing loss so that it can be identified and managed at early stage.
